Clinical and functional outcomes of hand surgery for recessive dystrophic epidermolysis bullosa

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dc.authoridzeybek, hakan/0000-0003-1525-9966
dc.contributor.authorCalavul, Abdulkadir
dc.contributor.authorCici, Hakan
dc.contributor.authorZeybek, Hakan
dc.contributor.authorKilic, Ali Ihsan
dc.date.accessioned2025-03-20T09:50:45Z
dc.date.available2025-03-20T09:50:45Z
dc.date.issued2025
dc.departmentİzmir Bakırçay Üniversitesi
dc.description.abstractRecessive dystrophic epidermolysis bullosa causes blistering and scarring of the hands, resulting in contractures fused web spaces and altered function. The aim of this study was to present the short- and mid-term clinical and functional results of a large case series of patients who underwent surgery for recessive dystrophic epidermolysis bullosa-related pseudosyndactyly. The study included 75 hands in 39 children (21 boys, 18 girls) with a mean age of 8 years (range, 4-15) and minimum follow-up of 1 year. Children were assessed with the Birmingham Epidermolysis Bullosa Severity Score Sheet and the ABILHAND-Kids questionnaire before operation and at final follow-up. There were varying degrees of recurrent scarring in all the hands by 24 months after operation. The ABILHAND-Kids questionnaire showed a significant improvement in ability to perform 17 of 21 tasks. In conclusion, despite recurrence that may develop in the short and mid term, surgical release can provide significant improvements in hand function.Level of Evidence: IV
dc.identifier.doi10.1177/17531934251313989
dc.identifier.issn1753-1934
dc.identifier.issn2043-6289
dc.identifier.pmid39989165
dc.identifier.scopusqualityQ2
dc.identifier.urihttps://doi.org/10.1177/17531934251313989
dc.identifier.urihttps://hdl.handle.net/20.500.14034/2294
dc.identifier.wosWOS:001428745900001
dc.identifier.wosqualityQ2
dc.indekslendigikaynakWeb of Science
dc.indekslendigikaynakPubMed
dc.language.isoen
dc.publisherSage Publications Ltd
dc.relation.ispartofJournal of Hand Surgery-European Volume
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanı
dc.rightsinfo:eu-repo/semantics/closedAccess
dc.snmzKA_WOS_20250319
dc.subjectEpidermolysis bullosa
dc.subjectpseudosyndactyly
dc.subjectsurgical treatment
dc.titleClinical and functional outcomes of hand surgery for recessive dystrophic epidermolysis bullosa
dc.typeArticle

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